From: Chronic granulomatous disease: a review of the infectious and inflammatory complications
Feature | US | European |
---|---|---|
Number (n) | 368 (259 XL/81 AR-CGD) | 429 (67% XL- and 33% AR-CGD) |
Pneumonia | 79% | 66% |
Suppurative adenitis | 53% | 50% |
Subcutaneous abscess | 52% | 53% |
Liver abscess | 27% | 32% |
Osteomyelitis | 25% | NA |
Sepsis | 18% | NA |
Gastric outlet obstruction | 15% | NA |
Urinary tract obstruction | 10% | NA |
Colitis/GI tract | 17% | 48% |
Mortality | 18% | NA |