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Table 3 Selected reports of HSP in adult patients

From: The clinical implications of adult-onset henoch-schonelin purpura

Patient (report)

Age/gender

Clinical/Labs

Histological diagnosis

Treatment

Outcome

1

24/M

Purpuric rash, arthritis, abdominal pain, Hematuria and proteinuria

Skin: LCV with IgA deposition Mesangial IgA deposition

Glucocorticoids Cyclophosphamide

Remission

2

68/M

Abdominal pain with diarrhea, purpuric rash, elevated sedimentation rate

Skin: LCV with IgA deposition

None

Spontaneous remission

3

77/M

Abdominal pain with diarrhea purpuric rash, hematuria, elevated IgA level and sedimentation rate

Skin: LCV with IgA deposition

Glucocorticoids Cyclophosphamide

Remission

4

69/M

Pustular rash, abdominal pain myocardial infarction

Endocapillary proliferative nephritis with IgA deposition subendocardial LCV

Glucocorticoids

Deceased

5

20/M,76/F, 67/F

Purpuric rash, arthralgia, hematuria hemoptysis, hypoxia, bilateral infiltrate

Skin: LCV with IgA deposition pulmonary interstitial fibrosis

Glucocorticoids

Remission

6

20/F

Purpuric rash, arthralgia, hematuria, proteinuria, seizure

Skin:LCV EEG: Transient focal abnormality MRI: normal

Glucocorticoids Dilantin

Remission

7*

56/M

Purpuric rash, crampy abdominal pain Hematuria, proteinuria, elevated IgA level

Skin: LCV

Colchicine

Remission

8*

57/M

Blistering rash, hematuria, Nephrotic syndrome

Skin: LCV Endocapillary proliferative nephritis mesangial IgA deposition

Glucocorticoids Colchicine

Partial remission

  1. LCV: Leukocytoclastic vasculitis; M = Male; F = Female
  2. * Cases described in this report