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Table 8 Differences between the XL and AR forms of CGD*

From: Chronic granulomatous disease: a review of the infectious and inflammatory complications

Feature XL CGD AR CGD
Family history of lupus 10% 3%
Age at diagnosis 3.01 years 7.81 years
Perirectal abscess 17% 7%
Suppurative adenitis 59% 32%
Bacteremia and/or fungemia 21% 10%
Gastric outlet obstruction 19% 5%
Urinary obstruction 11% 3%
Mortality (over 10 year observation) 21.2% 8.6%
  1. *Adapted from reference 30 (XL = x-linked; AR = autosomal recessive)