Table 8 Differences between the XL and AR forms of CGD*
From: Chronic granulomatous disease: a review of the infectious and inflammatory complications
Feature | XL CGD | AR CGD |
|---|---|---|
Family history of lupus | 10% | 3% |
Age at diagnosis | 3.01 years | 7.81 years |
Perirectal abscess | 17% | 7% |
Suppurative adenitis | 59% | 32% |
Bacteremia and/or fungemia | 21% | 10% |
Gastric outlet obstruction | 19% | 5% |
Urinary obstruction | 11% | 3% |
Mortality (over 10 year observation) | 21.2% | 8.6% |