From: X-linked agammaglobulinemia diagnosed late in life: case report and review of the literature
Patient 1 | Patient 2 | |
---|---|---|
Age | 64 | 46 |
WBC (cells/uL) | 8.3 (3.2–9.8) | 6.9 (5.0–10.2) |
Granulocytes (%) | 59 (42–75) | 68 (45–75) |
Lymphocytes (%) | 28 (20–51) | 18 (20–50) |
Monocytes (%) | 9.5 (0–12) | 12 (0–8) |
IgM (mg/dL) | 25 | 95 (50–300) |
IgG (mg/dL) | 360 | 260 (565–1765) |
IgA (mg/dL) | 27 | 16 (40–350) |
C3 (mg/dL) | ND | 129 (85–200) |
C4 (mg/dL) | ND | 23 (14–53) |
CH50 (U/ml) | ND | 51 (22–60) |
CD4+ (cells/uL) | 1023 (720–1440) | 624 (575–1070) |
CD8+ (cells/uL) | 979 (315–788) | 477 (190–860) |
NK (cells/uL) | ND | 135 (150–880) |
CD19+ (cells/uL) | 0 (113–495) | 0 (70–300) |
SPEP | Hypogammaglobulinemia | Hypogammaglobulinemia |
Pneumococcal responses | Impaired | Impaired |